Name
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3-hydroxyisobutyrate dehydrogenase | Cytological Location | 7p15.2 |
Brief Description | 3-hydroxyisobutyrate dehydrogenase |
Description | This gene encodes a mitochondrial 3-hydroxyisobutyrate dehydrogenase enzyme. The encoded protein plays a critical role in the catabolism of L-valine by catalyzing the oxidation of 3-hydroxyisobutyrate to methylmalonate semialdehyde. [provided by RefSeq, Nov 2011] |